Hemofilia A adquirida en el posparto: reporte de caso

Carlos H. Contreras-Pizarro; Gloria Chumpitaz-Anchiraico; Rosario Ticona Sanjínez; Carlos Peña-Diaz

doi:10.17843/rpmesp.2023.402.12593

Authors

Carlos H. Contreras-Pizarro Facultad de Medicina, Universidad Nacional Mayor de San Marcos, Lima, Perú https://orcid.org/0000-0001-7394-6284
Gloria Chumpitaz-Anchiraico Hospital Nacional Edgardo Rebagliati Martins, EsSalud, Lima, Perú https://orcid.org/0000-0003-3681-8587
Rosario Ticona Sanjínez Hospital Nacional Edgardo Rebagliati Martins, EsSalud, Lima, Perú https://orcid.org/0000-0003-4447-1878
Carlos Peña-Diaz Facultad de Medicina, Universidad Nacional Mayor de San Marcos, Lima, Perú. Hospital Nacional Edgardo Rebagliati Martins, EsSalud, Lima, Perú https://orcid.org/0000-0002-9223-7915

DOI:

https://doi.org/10.17843/rpmesp.2023.402.12593

Keywords:

Hemophilia A, Postpartum Period, Back Pain, Hematuria

Abstract

Acquired hemophilia A is a rare bleeding disorder worldwide, characterized by the presence of inhibitory
autoantibodies directed against a coagulation factor, most often factor VIII. There are several possible causes, and it can occur during the postpartum period. We present the case of a 34-year-old female patient with back pain, hematuria and a right gluteal hematoma, with no previous history of bleeding. She was transferred to the emergency department due to the extension of the hemorrhagic manifestations. Diagnosis was confirmed with the coagulation profile, mixing test and the assessment of factor VIII inhibitor tier. The case highlights the importance of considering this condition in a postpartum patient with persistent postoperative bleeding, extensive hematoma and no history of previous bleeding.

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